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CLN3 抗体 (AA 1-280)

CLN3 适用: 人 WB, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6219075
发货至: 中国
  • 抗原 See all CLN3 抗体
    CLN3 (Ceroid-Lipofuscinosis, Neuronal 3 (CLN3))
    抗原表位
    • 12
    • 3
    • 3
    • 2
    • 1
    • 1
    • 1
    • 1
    AA 1-280
    适用
    • 24
    • 19
    • 14
    • 3
    • 3
    宿主
    • 26
    • 1
    克隆类型
    • 26
    • 1
    多克隆
    标记
    • 12
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    This CLN3 antibody is un-conjugated
    应用范围
    • 24
    • 8
    • 3
    • 2
    Western Blotting (WB), Immunohistochemistry (IHC)
    序列
    MGGCAGSRRR FSDSEGEETV PEPRLPLLDH QGAHWKNAVG FWLLGLCNNF SYVVMLSAAH DILSHKRTSG NQSHVDPGPT PIPHNSSSRF DCNSVSTAAV LLADILPTLV IKLLAPLGLH LLPYSPRVLV SGICAAGSFV LVAFSHSVGT SLCGVVFASI SSGLGEVTFL SLTAFYPRAV ISWWSSGTGG AGLLGALSYL GLTQAGLSPQ QTLLSMLGIP ALLLASYFLL LTSPEAQDPG GEEEAESAAR QPLIRTEAPE SKPGSSSSLS LRERWTVFKG
    交叉反应
    人, 小鼠, 大鼠
    产品特性
    Polyclonal Antibodies
    纯化方法
    Affinity purification
    免疫原
    Recombinant fusion protein containing a sequence corresponding to amino acids 1-280 of human CLN3 (NP_001035897.1).
    亚型
    IgG
    Top Product
    Discover our top product CLN3 Primary Antibody
  • 应用备注
    WB,1:500 - 1:2000,IHC,1:50 - 1:100
    限制
    仅限研究用
  • 缓冲液
    PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
    储存液
    Sodium azide
    注意事项
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    储存条件
    -20 °C
    储存方法
    Store at -20°C. Avoid freeze / thaw cycles.
  • 抗原
    CLN3 (Ceroid-Lipofuscinosis, Neuronal 3 (CLN3))
    别名
    CLN3 (CLN3 产品)
    别名
    BTS antibody, JNCL antibody, AI323623 antibody, zgc:92244 antibody, GB12798 antibody, MGC80041 antibody, bts antibody, CLN3, battenin antibody, ceroid lipofuscinosis, neuronal 3, juvenile (Batten, Spielmeyer-Vogt disease) antibody, ceroid-lipofuscinosis, neuronal 3 antibody, battenin antibody, ceroid-lipofuscinosis, neuronal 3 L homeolog antibody, uncharacterized LOC467935 antibody, CLN3 antibody, Cln3 antibody, cln3 antibody, PTRG_05620 antibody, LOC410860 antibody, cln3.L antibody, LOC467935 antibody
    背景
    This gene encodes a protein that is involved in lysosomal function. Mutations in this, as well as other neuronal ceroid-lipofuscinosis (CLN) genes, cause neurodegenerative diseases commonly known as Batten disease or collectively known as neuronal ceroid lipofuscinoses (NCLs). Many alternatively spliced transcript variants have been found for this gene.,CLN3,BTN1,BTS,JNCL,battenin,Cell Biology & Developmental Biology,Apoptosis,Neuroscience,Neurodegenerative Diseases,CLN3
    分子量
    28 kDa/34 kDa/37 kDa/42 kDa/45 kDa/47 kDa
    基因ID
    1201
    UniProt
    Q13286
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