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HPS3 抗体 (C-Term)

HPS3 适用: 人 WB 宿主: 山羊 Polyclonal unconjugated
产品编号 ABIN374450
发货至: 中国
  • 抗原 See all HPS3 抗体
    HPS3 (Hermansky-Pudlak Syndrome 3 (HPS3))
    抗原表位
    • 8
    • 8
    • 6
    • 2
    • 2
    • 1
    • 1
    C-Term
    适用
    • 23
    • 3
    • 3
    • 2
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    宿主
    • 21
    • 1
    • 1
    山羊
    克隆类型
    • 23
    多克隆
    标记
    • 13
    • 2
    • 2
    • 2
    • 2
    • 2
    This HPS3 antibody is un-conjugated
    应用范围
    • 23
    • 15
    • 4
    • 2
    • 2
    • 2
    Western Blotting (WB)
    序列
    PYLLYCSRKK PLT
    特异性
    This antibody recognizes HPS3/Cocoa
    交叉反应 (详细)
    Species reactivity (tested):Human.
    纯化方法
    Ammonium Sulphate Precipitation followed by antigen Affinity Chromatography using the immunizing peptide.
    免疫原
    Peptide from the C Terminus of the protein sequence according to NP_115759
    Top Product
    Discover our top product HPS3 Primary Antibody
  • 应用备注
    Peptide ELISA: > 1/32,000. Western Blot: 1-3 μg/mL. Detects a band of Approx 110 kDa in A431 cell lysate(Predicted Molecular Weight: 114 kDa).
    Other applications not tested.
    Optimal dilutions are dependent on conditions and should be determined by the user.
    限制
    仅限研究用
  • 浓度
    0.5 mg/mL
    缓冲液
    Tris saline, pH 7.3 containing 0.02 % Sodium Azide as preservative and 0.5 % BSA as stabilizer.
    储存液
    Sodium azide
    注意事项
    This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    注意事项
    Avoid repeated freezing and thawing.
    储存条件
    -20 °C
    储存方法
    Store the antibody (in aliquots) at -20 °C.
  • 抗原
    HPS3 (Hermansky-Pudlak Syndrome 3 (HPS3))
    别名
    HPS3 (HPS3 产品)
    别名
    SUTAL antibody, HPS3 antibody, coa antibody, HPS3, biogenesis of lysosomal organelles complex 2 subunit 1 antibody, HPS3, biogenesis of lysosomal organelles complex 2 subunit 1 L homeolog antibody, Hermansky-Pudlak syndrome 3 antibody, HPS3 antibody, hps3.L antibody, Hps3 antibody
    背景
    HPS3 is involved in early stages of melanosome biogenesis and maturation. Defects in HPS3 are the cause of the cocoa (coa) mutant, and of Hermansky-Pudlak syndrome type 3 (HPS3). HPS3 is an autosomal recessive disorder, characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS.Synonyms: Hermansky-Pudlak syndrome 3
    基因ID
    84343
    NCBI登录号
    NP_115759
    UniProt
    Q969F9
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