anti-NFU1 Iron-Sulfur Cluster Scaffold Homolog (S. Cerevisiae) (NFU1) 抗体

NFU1 encodes a protein that is localized to mitochondria and plays a critical role in iron-sulfur cluster biogenesis. 再加上,我们可以发NFU1 Iron-Sulfur Cluster Scaffold Homolog (S. Cerevisiae) 蛋白 (4)和数多这个蛋白质的别的产品。

列出全部抗体 基因 基因ID UniProt
NFU1 27247 Q9UMS0
NFU1 56748 Q9QZ23
NFU1    

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产品编号 适用 宿主 标记 应用范围 图像 规格 供应商 交付 价格 详细
非结合性 IHC, WB Immunohistochemical analysis of NFU1 staining in mouse brain formalin fixed paraffin embedded tissue section. The section was pre-treated using heat mediated antigen retrieval with sodium citrate buffer (pH 6.0). The section was then incubated with the an Western blot analysis of NFU1 expression in SW480 (A), mouse liver (B), mouse heart (C), rat liver (D), rat heart (E) whole cell lysates. 200 μL Log in to see 7至8个工作日
¥3,981.76
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非结合性 ICC, IF, IHC, IHC (p) Immunohistochemistry-Paraffin: NFU1 iron-sulfur cluster scaffold homolog (S. cerevisiae) Antibody [NBP2-48647] - Staining of human vulva/anal skin shows strong cytoplasmic positivity in epidermal cells. Immunocytochemistry/Immunofluorescence: NFU1 iron-sulfur cluster scaffold homolog (S. cerevisiae) Antibody [NBP2-48647] - Analysis of human cell line U-2 OS shows positivity in cytoplasm & nucleus but excluded from the nucleoli. 0.1 mL Log in to see 28至35个工作日
¥3,591.24
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通过反应活性、应用领域、克隆类型和共轭标记 NFU1 抗体

特性 应用范围 宿主 克隆类型
Human ,


Mouse (Murine)


Rat (Rattus)


更多抗NFU1 Iron-Sulfur Cluster Scaffold Homolog (S. Cerevisiae)的相互作用对抗体

Human NFU1 Iron-Sulfur Cluster Scaffold Homolog (S. Cerevisiae) (NFU1) interaction partners

  1. a direct role for human Nfu in the process of [2Fe-2S] cluster trafficking and delivery

  2. Analysis of protein stability and oligomeric state demonstrates that the Gly208Cys mutant increases the propensity to dimerize and perturbs the secondary structure composition. These changes appear to underlie the severely decreased ability of mutant NFU1 to accept an Fe/S cluster from physiologically relevant sources.

  3. Study used NMR spectroscopy and small-angle X-ray scattering data to determine the 3D structure of human mitochondrial NFU1 in its apo (显示 C9orf3 抗体)- and iron-sulfur cluster-containing holo-form. Apo (显示 C9orf3 抗体)- NFU1 is monomeric, whereas holo-NFU1 consists of a trimer of three [4Fe-4S] cluster-linked dimers.

  4. a leaky splicing regulation due to a splice site mutation (c.545+5G>A) that produces small amounts of wild type NFU1 mRNA that might result in enough protein to partially lipoylate and restore the activity of lipoic acid-dependent enzymes and the assembly and activity of complex I.

  5. A new NFU1 mutation is reported in a patient presenting with a milder phenotype characterized by a later onset, a slowly progressive spastic paraparesis with relapsing-remitting episodes, mild cognitive impairment and a long survival.

  6. This study provides new insights into the molecular bases of NFU1 disease.

  7. A fatal mitochondrial disease is associated with defective NFU1 function in the maturation of a subset of mitochondrial Fe-S proteins

  8. Mutations in iron-sulfur cluster scaffold genes NFU1 and BOLA3 (显示 BOLA3 抗体) cause a fatal deficiency of multiple respiratory chain and 2-oxoacid dehydrogenase enzymes [case report]

  9. Analyses of genomic DNA, transcripts, and translation products indicate that alternative splicing of a common pre-mRNA results in synthesis of two Nfu isoforms with distinct subcellular localizations.

  10. Laforin (显示 EPM2A 抗体) interacts with HIRIP5.

NFU1 Iron-Sulfur Cluster Scaffold Homolog (S. Cerevisiae) (NFU1) 抗原简介

蛋白简介

This gene encodes a protein that is localized to mitochondria and plays a critical role in iron-sulfur cluster biogenesis. The encoded protein assembles and transfers 4Fe-4S clusters to target apoproteins including succinate dehydrogenase and lipoic acid synthase. Mutations in this gene are a cause of multiple mitochondrial dysfunctions syndrome-1, and pseudogenes of this gene are located on the short arms of chromosomes 1 and 3. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene.

Gene names and symbols associated with NFU1

  • NFU1 iron-sulfur cluster scaffold homolog (S. cerevisiae) (NFU1) 抗体
  • NFU1 iron-sulfur cluster scaffold homolog (S. cerevisiae) (Nfu1) 抗体
  • 0610006G17Rik 抗体
  • CGI-33 抗体
  • HIRIP 抗体
  • Hirip5 抗体
  • MMDS1 抗体
  • Nfu 抗体
  • NifU 抗体
  • NIFUC 抗体

Protein level used designations for NFU1

HIRA-interacting protein 5 , NFU1 iron-sulfur cluster scaffold homolog, mitochondrial , NifU-like C-terminal domain containing , iron-sulfur cluster scaffold protein , histone cell cycle regulation defective interacting protein 5 , mHIRIP5

GENE ID SPECIES
27247 Homo sapiens
56748 Mus musculus
anti-NFU1 Iron-Sulfur Cluster Scaffold Homolog (S. Cerevisiae) (NFU1) 抗体 精选生产商
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