anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) 抗体

MCCC1 encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. 再加上,我们可以发Methylcrotonoyl-CoA Carboxylase 1 (Alpha) 蛋白 (7)Methylcrotonoyl-CoA Carboxylase 1 (Alpha) 试剂盒 (1)和数多这个蛋白质的别的产品。

列出全部抗体 基因 基因ID UniProt
MCCC1 56922 Q96RQ3
MCCC1 294972 Q5I0C3
MCCC1 72039 Q99MR8
How to order from antibodies-online
  • +1 877 302 8632
  • +1 888 205 9894 (toll-free)
  • 在线下订单
  • orders@antibodies-online.cn

antibodies-online.cn销售最多的anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) 抗体

Showing 10 out of 35 products:

产品编号 适用 宿主 标记 应用范围 图像 规格 供应商 交付 价格 详细
小鼠 非结合性 ELISA, WB Detection limit for recombinant GST tagged MCCC1 is approximately 0.1 ng/mL as a capture antibody. 0.1 mg Log in to see 8至11个工作日
$450.00
详细
非结合性 WB MCCC1 Antibody (Center) (ABIN651863) western blot analysis in mouse liver tissue lysates (15 µg/lane). This demonstrates the MCCC1 antibody detected MCCC1 protein (arrow). 400 μL Log in to see 10至11个工作日
$324.50
详细
非结合性 WB Western blot analysis of extracts of Jurkat and mouse kidney cells, using MCCC1 antibody. 100 μL Log in to see 16 Days
$323.13
详细
小鼠 非结合性 ELISA, WB Detection limit for recombinant GST tagged MCCC1 is approximately 0.1ng/ml as a capture antibody. Western Blot detection against Immunogen (36.74 KDa) . 100 μg Log in to see 11至12个工作日
$430.00
详细
非结合性 ICC, IF, IHC, IHC (p), WB Immunocytochemistry/Immunofluorescence: MCCC1 Antibody [NBP1-81254] - Staining of human cell line U-2 OS shows positivity in mitochondria. Immunohistochemistry-Paraffin: MCCC1 Antibody [NBP1-81254] - Immunohistochemical staining of human cerebral cortex shows strong cytoplasmic positivity in neuronal cells. 0.1 mL Log in to see 10至13个工作日
$439.69
详细
非结合性 WB Western blot analysis in mouse liver tissue lysates (15ug/lane).This demonstrates the detected MCCC1 protein (arrow). 400 μL Log in to see 2至3个工作日
$515.63
详细
非结合性 ELISA, WB   200 μL Log in to see 7至9个工作日
$793.83
详细
APC ELISA, WB   200 μL Log in to see 7至9个工作日
$1,013.83
详细
Alkaline Phosphatase (AP) ELISA, WB   200 μL Log in to see 7至9个工作日
$1,013.83
详细
PE ELISA, WB   200 μL Log in to see 7至9个工作日
$1,013.83
详细

通过反应活性、应用领域、克隆类型和共轭标记 MCCC1 抗体

特性 应用范围 宿主 克隆类型 标记
Human
,
,
, , , , ,
Rat (Rattus)


Mouse (Murine)


, , , , ,

更多抗Methylcrotonoyl-CoA Carboxylase 1 (Alpha)的相互作用对抗体

Human Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) interaction partners

  1. This study reports data mainly obtained from the Portuguese newborn screening program collected over a ten-year period. Analysis of the MCCC1 and MCCC2 (显示 MCCC2 抗体) genes yielded 26 previously unreported mutations and a variant of clinically unknown significance.

  2. Our study provides strong support for the susceptibility role of RAB7L1/NUCKS1 rs823118 and MCCC1 rs12637471 in sporadic Parkinson's disease in a Han Chinese population

  3. Novel mutations in MCCC1 gene were identified in Chinese population. The expression profiles of two splice mutations (c.639+2T>A and c.639+5G>T) were also characterized.

  4. Four new point mutations were detected in the MCCC1 gene in patients with maternal 3-methylcrotonyl coenzyme deficiency.

  5. This study demonistrated that Mainland China demonstrates that MCCC1/LAMP3 (显示 CD63 抗体) (rs11711441) is associated with a lower risk of Parkinson's disease.

  6. 3-methylcrotonyl-CoA carboxylase (显示 MCCC2 抗体) inhibition has a role in increased excretion of 3-hydroxyisovaleric acid in valproate-treated patients

  7. Mutation in 3-methylcrotonyl CoA carboxylase 1 gene is associated with 3-methylcrotonyl-CoA carboxylase (显示 MCCC2 抗体) deficiency.

  8. study reports eight different mutant alleles of MCCC1 or MCCC2 (显示 MCCC2 抗体) including six novel mutations in Korean patients with 3-methylcrotonyl-CoA carboxylase (显示 MCCC2 抗体) (MCC (显示 MCC 抗体)) deficiency

  9. identified two novel MCCA and four novel MCCB mutant alleles from five MCC (显示 MCC 抗体)-deficient patients

  10. factors other than the genotype at the MCCA and MCCB loci have a major influence on the phenotype of MCC (显示 MCC 抗体) deficiency

Arabidopsis thaliana Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) interaction partners

  1. Studies indicate that mutations in either 3-methylcrotonyl CoA carboxylase (显示 MCCC2 抗体) MCCA (At1g03090) or MCCB (显示 MCCC2 抗体) (At4g34030) block mitochondrial Leu catabolism, as inferred from the increased accumulation of Leu.

Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) 抗原简介

蛋白简介

This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.

Gene names and symbols associated with MCCC1

  • methylcrotonoyl-CoA carboxylase 1 (MCCC1) 抗体
  • methylcrotonoyl-CoA carboxylase 1 (Mccc1) 抗体
  • methylcrotonyl-CoA carboxylase alpha chain (MCCA) 抗体
  • methylcrotonoyl-Coenzyme A carboxylase 1 (alpha) (Mccc1) 抗体
  • 1810045E08Rik 抗体
  • 2310058B18Rik 抗体
  • MCC-B 抗体
  • Mcca 抗体
  • MCCalpha 抗体
  • R75106 抗体

Protein level used designations for MCCC1

3-methylcrotonyl-CoA carboxylase 1 , 3-methylcrotonyl-CoA carboxylase biotin-containing subunit , 3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha , MCCase subunit alpha , methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial , methylcrotonoyl-Coenzyme A carboxylase 1 (alpha)

GENE ID SPECIES
56922 Homo sapiens
294972 Rattus norvegicus
838362 Arabidopsis thaliana
72039 Mus musculus
anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) 抗体 精选生产商
您还需要查找其他产品吗?